Epithelioid sarcoma is a rare type of tumor that primarily affects young men and accounts for less than 1% of all soft tissue sarcomas. In this case, a patient diagnosed with epithelioid sarcoma and systemic metastases presented with complaints of decreased vision and eye pain. Examination revealed a mass lesion involving the conjunctiva, iris and lens, accompanied by conjunctival hyperemia, corneal edema and hyphema. Ocular metastasis was suspected, and samples were obtained through excisional biopsy of the conjunctival nodule and aspiration of fluid from the anterior chamber. Pathological examination confirmed that the conjunctival nodule represented an ocular metastasis of epithelioid sarcoma. Although there are reported cases of primary orbital epithelioid sarcoma, we present this report because it demonstrates a unique example of extra-orbital primary disease with subsequent ocular metastasis.
Keywords: Epithelioid sarcoma, ocular metastasis, conjunctival nodule